Ontological Term Details

Compound
FDB021910 (L-Palmitoylcarnitine)
Term
Very long chain acyl-coa dehydrogenase deficiency
Definition
A lipid metabolism disorder that is characterized by deficiency of the enzyme very long chain acyl-coa dehydrogenase that results in the inability to convert very long chain fatty acids. (do).
Parent Term
Health condition
Parent Definition
A health effect that consists on short or long-term disease, condition, disorder, syndrome or constant abnormality.
Synonyms
  • Vlcad
  • Vlchad
  • Other Compounds Mapped to 'Very long chain acyl-coa dehydrogenase deficiency'
  • FDB022183 (Isovalerylcarnitine)
  • FDB021910 (L-Palmitoylcarnitine)
  • FDB023615 (Tetradecanoylcarnitine)
  • FDB022928 (Dodecanoylcarnitine)
  • FDB023884 (trans-Hexadec-2-enoyl carnitine)
  • FDB022192 (Hexanoylcarnitine)
  • FDB022246 (L-Octanoylcarnitine)
  • FDB022078 (5-Tetradecenoic acid)
  • FDB022162 (Decanoylcarnitine)
  • References

      • 9034211
      • 29140435