Search Results for compound
Searching compound for heptanol coa returned 1526 results.
Displaying compounds 276 - 300 of 1526 in total
[(2R)-2-hydroxy-3-(octadec-9-enoyloxy)propoxy]phosphonic acid
Matched description: … Decanoyl-CoA (n-C10:0CoA), also known as decanoyl-CoA or S-decanoate, belongs to the class of organic ... Decanoyl-CoA (n-C10:0CoA) is a strong basic compound (based on its pKa). …
FDB021963
52320-67-9
2-(2-methylbutanamido)acetic acid
Matched description: … with acetyl-CoA catalyzed by 3-oxoacyl-CoA thiolases. ... + glycine < -- > CoA + N-acylglycine. ... glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction:
acyl-CoA …
FDB023568
505-90-8
(4Z)-dec-4-enoic acid
Matched description: … acyl-CoA dehydrogenase deficiency (VLCADD) (PMID 11486898) [HMDB] ... amounts in liver, skeletal muscle and heart obtained post mortem from patients with medium-chain acyl-CoA ... dehydrogenase deficiency (MCADD), multiple acyl-CoA dehydrogenase deficiency (MADD) and very long-chain …
FDB028791
884-33-3
(2S)-2-benzylbutanedioic acid
Matched description: … It is then converted to Benzylsuccinyl-CoA via the enzyme benzylsuccinate CoA-transferase BbsE subunit ... (R)-2-Benzylsuccinate is an aromatic compounds that is an intermediate in Benzoate degradation via CoA ... Benzoyl-CoA is the most important of these intermediates since a large number of compounds, including …
FDB022716
3586-58-1
2-methylidenebutanoic acid
Matched description: … thiolase deficiency and methylmalonyl-CoA mutase deficiency) (PMID 1016232) [HMDB] ... variably increased in defects of isoleucine oxidation at distal steps in the catabolic pathway (3-oxoacyl-CoA …
FDB022208
15926-18-8
2-(2-methylpropanamido)acetic acid
Matched description: … Isobutyryl-CoA dehydrogenase deficiency is a disorder caused by the deficiency of isobutyryl-CoA dehydrogenase ... with isobutyryl-CoA dehydrogenase deficiency. ... glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction:
acyl-CoA …
FDB022837
13870-90-1
Matched description: … Methylmalonyl-CoA mutase catalyzes the conversion of L-methylmalonyl-CoA to succinyl-CoA and uses adenosylcobalamin ... the predominant form in the liver; it acts as a coenzyme in the reaction catalyzed by methylmalonyl-CoA ... the predominant form in the liver; it acts as a coenzyme in the reaction catalyzed by methylmalonyl-CoA …
FDB022090
5746-90-7
(2E)-3-methylpent-2-enedioic acid
Matched description: … 3-Methylglutaconic acid is an intermediate (as the CoA thioester) in the leucine degradative pathway ... well as the mevalonate shunt, a pathway that links isoprenoid metabolism with mitochondrial acetyl-CoA ... (PMID: 7603789)
3-methylglutaconyl-CoA hydratase is involved in the metabolism process of 3-methylglutaconic …
FDB023226
2382-59-4
2-methyl-3-oxobutanoic acid
Matched description: … Methylacetoacetic acid is a metabolite that has an increased excretion in patients with acetoacetyl-CoA ... Thiolases are CoA-dependent enzymes which catalyze the formation of a carbon-carbon bond in a Claisen ... and its reverse reaction via a thiolytic degradation mechanism. mitochondrial acetoacetyl-coenzyme A (CoA …
FDB021937
105-45-3
methyl 3-oxobutanoate
Matched description: … carboxylase (PMID 630060), and after isoleucine loading in the diagnosis of 2-methylacetoacetyl-CoA ... Methylacetoacetic acid has been identified in the urine of patients with an inherited deficiency of propionyl-CoA …
FDB022225
625-08-1
3-hydroxy-3-methylbutanoic acid
Matched description: … in several inherited disorders such as Dihydrolipoamide dehydrogenase Deficiency, 3-Methylcrotonyl-CoA ... carboxylase 1 deficiency, 3-Hydroxy-3-methylglutaryl-CoA lyase deficiency (3-hydroxy-3-methylglutaryl ... -CoA lyase Deficiency, Biotinidase deficiency multiple carboxylase deficiency late-onset , Late onset …
FDB021826
18534-66-2
lambda2-cobalt(2+) ion 3-[13-(3-azanidyl-3-oxopropyl)-4-{2-[(2-{[hydroxy({[4-hydroxy-2-(hydroxymethyl)-5-(5-methyl-1-methylidene-3H-1lambda5,3-benzodiazol-3-yl)oxolan-3-yl]oxy})phosphoryl]oxy}propyl)-C-hydroxycarbonimidoyl]ethyl}-18-[2-(C-hydroxycarbonimidoyl)ethyl]-3,14,19-tris[(C-hydroxycarbonimidoyl)methyl]-1,4,6,9,9,14,16,19-octamethyl-20,21,22,23-tetraazapentacyclo[15.2.1.1^{2,5}.1^{7,10}.1^{12,15}]tricosa-5(23),6,10(22),11,15(21),16-hexaen-8-yl]propanecarboximidate
Matched description: … mutase, which catalyzes the rearrangement of methylmalonyl-CoA to form succinyl-CoA. ... cob(I)alamin to the adenosylcobalamin co-factor required for the functional activity of methylmalonyl-CoA ... of a methyl group from methyltetrahydrofolate to homocysteine to form methionine, and methylmalonyl-CoA …
FDB022860
298-08-8
1-aminopropan-2-one
Matched description: … when the ratio acetyl-CoA/CoA increases in nutritional deprivation (e.g., in diabetes) the enzyme produces ... Threonine dehydrogenase catalyzes the oxidation of threonine by NAD+ to glycine and acetyl-CoA (5), but …
FDB003282
3724-65-0
but-2-enoic acid
Matched description: … But-2-enoic acid is fatty acid formed by the action of fatty acid synthases from acetyl-CoA and malonyl-CoA …
FDB022336
60317-54-6
7-[(carboxymethyl)carbamoyl]heptanoic acid
Matched description: … + glycine < -- > CoA + N-acylglycine
Suberylglycine is a dicarboxylic acid. ... glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction:
acyl-CoA ... It can be used for the diagnosis of hereditary medium-chain acyl-CoA dehydrogenase deficiency (PMID 2775902 …
FDB024132
13015-87-7
(acetyloxy)({[(2R,3S,4R,5R)-5-(6-amino-9H-purin-9-yl)-3,4-dihydroxyoxolan-2-yl]methoxy})phosphinic acid
Matched description: … Acetyl adenylate is an intermediate in acetyl-CoA synthesis. ... It is converted from acetate via the enzyme acetyl-CoA synthetase. …
FDB021905
516-05-2
2-methylpropanedioic acid
Matched description: … CoA. ... This metabolic disease is attributed to a block in the enzymatic conversion of methylmalonyl CoA to succinyl …
3-[(4,8-dimethylnonanoyl)oxy]-4-(trimethylazaniumyl)butanoate
Matched description: … and propionyl-CoA. ... Both phytanic acid and pristanic acid are initially oxidized in peroxisomes to 4,8-dimethylnonanoyl-CoA ... (DMN-CoA) which is then transported to the mitochondria for full oxidation to CO(2) and H(2)O. …
FDB023896
28047-15-6
(2S)-4-carbamoyl-2-(2-phenylacetamido)butanoic acid
Matched description: … + L-glutamine CoA + alpha-N-phenylacetyl-L-glutamine
Thus, the two substrates of this enzyme are phenylacetyl-CoA ... Phenylacetyl CoA and glutamine react to form phenylacetyl glutamine and Coenzyme A. ... and L-glutamine, whereas its two products are CoA and alpha-N-phenylacetyl-L-glutamine. …
FDB028830
13023-70-6
5-aminopentanamide
Matched description: … of glutaryl-CoA to carbon dioxide and acetyl-CoA have been demonstrated in Pseudomonas fluorescens [ ... Activation of glutarate to glutaryl-CoA by an as yet uncharacterized reaction(s) and further metabolism …
FDB022843
853728-01-5
(3S)-3-[(2-carboxyacetyl)oxy]-4-(trimethylazaniumyl)butanoate
Matched description: … into the mitochondria and failure of the mitochondrial respiratory chain at complex 11 and malonyl-CoA ... Malonylcarnitine has also been found to accumulate in some newborns with medium-chain acyl-CoA dehydrogenase …
FDB027893
926-61-4
3-oxopropanoic acid
Matched description: … deficiency show that malonic semialdehyde is directly converted into acetyl-CoA in man. ... Studies done on these pathways in cultured cells from a patient with mitochondrial malonyl-CoA decarboxylase …
FDB022984
7540-70-7
4,8-dimethylnonanoic acid
Matched description: … thioesterase and transported to the mitochondrion, followed by reactivation to its CoA-ester inside ... undergoes three cycles of β-oxidation) and then exported to the mitochondria or hydrolyzed by an acyl-CoA …
FDB027868
77877-35-1
(3R)-3-hydroxyhexanoic acid
Matched description: … and malonyl-CoA precursors. ... )==-3-Hydroxyhexanoic acid is a fatty acid formed by the action of fatty acid synthases from acetyl-CoA …
FDB022014
4374-62-3
2-(hydroxymethyl)butanoic acid
Matched description: … -Ethylhydracrylic acid (2-methylbutyrylglycine; 2-MBG) is the hallmark of short/branched-chain acyl-CoA ... thiolase deficiency and methylmalonyl-CoA mutase deficiency) and is diminished when proximal steps of ... variably increased in defects of isoleucine oxidation at distal steps in the catabolic pathway (3-oxoacyl-CoA …