Search Results for compound

Matched description: … of patients with hereditary medium-chain acyl-CoA dehydrogenase (MCAD) deficiency (PMID 2775902). ... glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction: acyl-CoA ... + glycine < -- > CoA + N-acylglycine Hexanoylglycine is a fatty acid metabolite, it appears in the urine …

Matched description: … thiolase (EC 2.3.1.9, acetyl-CoA C-acetyltransferase) deficiency (ACAT, OMIM 607809). ... Methylglutaconic acid is found in the urine of patients with organic aciduria from 2-methylacetoacetyl-CoA …

Matched description: … and malonyl-CoA precursors. ... oil trans-Hex-2-enoic acid is fatty acid formed by the action of fatty acid synthases from acetyl-CoA …

Matched description: … 3-Oxohexanoic acid is fatty acid formed by the action of Fatty acid synthases from acetyl-CoA and malonyl-CoA …

Matched description: … 3-Oxo-Octanoic acid is fatty acid formed by the action of acid synthases from acetyl-CoA and malonyl-CoA …

Matched description: … Accumulates in patients with deficiency of alpha-methylacyl-CoA racemase [HMDB] …

Matched description: … glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction: acyl-CoA ... + glycine < -- > CoA + N-acylglycine The level of propionylglycine is elevated in patients with propionic ... acidemia, which is an inherited deficiency of propionyl-CoA carboxylase. …

Matched description: … <=> Hydroxyphenylacetylglycine + CoA, catalyzed by acyltransferase enzymes (EC 2.3.1.-). ... + glycine < -- > CoA + N-acylglycine Hydroxyphenylacetylglycine is an endogenous human metabolite. ... glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction: acyl-CoA …

Matched description: … (R)-2-Hydroxycaprylic acid is an inhibitor of the medium chain acyl-CoA synthetase. [HMDB] …

Matched description: … + glycine < -- > CoA + N-acylglycine The detection of phenylpropionylglycine in urine after an oral ... load of phenylpropionic acid can be used to diagnose deficiency of medium-chain acyl-CoA dehydrogenase ... glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction: acyl-CoA …

Matched description: … glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction: acyl-CoA ... + glycine < -- > CoA + N-acylglycine Urinary excretion of 3-phenylpropionylglycine is a diagnostic marker ... for medium-chain acyl-CoA dehydrogenase deficiency. 3-phenylpropionylglycine is derived from 3-phenylpropionic …

Matched description: … It acts as a competitive inhibitor of HMG CoA reductase (hydroxymethylglutaryl CoA reductases); In medicine …

Matched description: … This compound is a regulatory oxysterol which can alter HMG-CoA reductase activity when minor changes …

Matched description: … Pseudoecgonine is a steroisomer of ecgonine and may be conjugated to CoA to form Pseudoecgonyl-CoA through …

Matched description: … Recombinantly expressed hGLYATL2 efficiently conjugated oleoyl-CoA, arachidonoyl-CoA, and other medium …

Matched description: … (E)-2-Hexenoic acid is fatty acid formed by the action of fatty acid synthases from acetyl-CoA and malonyl-CoA …

Matched description: … + glycine < -- > CoA + N-acylglycine. 3-Methylcrotonylglycine is a normal amino acid metabolite found ... glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction: acyl-CoA ... metabolite are found in patients suffering from leucine catabolic disorders, such as 3-methylcrotonyl-CoA …

Matched description: … glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction: acyl-CoA ... IVA (OMIM/ McKusick 243500) is an autosomal recessive disorder caused by mutations in the isovaleryl-CoA ... + glycine < -- > CoA + N-acylglycine Isovalerylglycine is a byproduct of the catabolism of the aminoacid …

Matched description: … 2-Acetolactate is involved in the butanoate metabolism and pantothenate and CoA biosynthesis pathways ... In the pantothenate and CoA pathway, 2-Acetolactate is irreversibly created from pyruvate by acetolactate …

Matched description: … Dodecanoylcarnitine is an acylcarnitine is present in fatty acid oxidation disorders such as long-chain acyl CoA …

Matched description: … + glycine < -- > CoA + N-acylglycine Nicotinuric acid is the major detoxification product of nicotinic ... glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction: acyl-CoA …

Matched description: … intermediate of unsaturated fatty acid metabolism found in plasma of patients with very-long-chain acyl-CoA …

Matched description: … fatty acid oxidation disorders and differentiation between biochemical phenotypes of medium-chain acyl-CoA …

Matched description: … glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction: acyl-CoA ... + glycine < -- > CoA + N-acylglycine A complex of amino acid protein that helps kill microbes, and protects …

Matched description: … glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction: acyl-CoA ... + glycine < -- > CoA + N-acylglycine Valerylglycine are identified based on their liquid chromatographic-atmospheric …